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Peutz-Jeghers Syndrome - JMI ArticlesArticles from our collection about Peutz-Jeghers Syndrome published during the 1970sTitle: Three varieties of hereditary intestinal polyposis Authors: Santos MJ;Krush AJ;Cameron JL; Abstract: Link: Click to read article Title: [Peutz-Jeghers syndrome] Authors: Baillot R;Le Gresley LP;Girard RM; Abstract: Link: Click to read article Title: [Peutz-Jeghers syndrome] Authors: Baillot R;Le Gresley LP;Girard RM; Abstract: Link: Click to read article Title: Prevention of intussusception in Peutz-Jeghers syndrome Authors: Holt RW; Abstract: Peutz-Jeghers syndrome is a familial disease characterized by mucocutaneous pigmentation and intestinal polyposis. Small-intestinal intussusception is a common complication. Preservation otion technique to prevent intussusception is described Link: Click to read article Title: Hamartomatous polyps in Peutz-Jeghers syndrome Authors: Williams GT;Bussey HJ;Morson BC; Abstract: Link: Click to read article Title: Enteritis cystica profunda Authors: Kyriakos M;Condon SC; Abstract: In addition to hamartomatous polyps of the small intestine, a patient with Peutz-Jeghers disease had gross and microscopic lesions of the ileum that were analogous to colitis cystica profunda in the large intestine and rectum. To the authors' knowledge, this is the first such case in an adult to be reported. They suggest the designation, 'enteritis cystica profunda.' The histology of the lesions and their association with a disease known to produce hamartomatous lesions lend support to the proposition that some cases of colitis cystica are also hamartamatous. It is also believed that some reported cases of small-intestinal adenocarcinoma in patients with Peutz-Jeghers syndrome are in reality examples of the benign process of enteritis cystica profunda Link: Click to read article Title: Peutz-Jeghers syndrome: case presentation Authors: Costa J; Abstract: The different aspects of the Peutz-Jeghers syndrome are discussed following a case presentation of a 36-year-old woman with Peutz-Jeghers syndrome, sex cord tumor with annular tubules of Scully, mucinous metaplasia of tubal epithelium, and adenocarcinoma of the endocervix. The latter two findings have not been described with the syndrome and an attempt is made to correlate them with Peutz-Jeghers syndrome Link: Click to read article Title: Involution of mucocutaneous pigmentation of the Peutz-Jeghers syndrome Authors: Keeling PW;Aston N;Anderson HJ; Abstract: Link: Click to read article Title: Peutz-jeghers syndrome Authors: Therriault CA;McKenna JE; Abstract: Link: Click to read article Title: Peutz-jeghers syndrome Authors: Therriault CA;McKenna JE; Abstract: Link: Click to read article Title: Radiological case of the month Authors: Gwinn JL;Lee FA; Abstract: Link: Click to read article Title: The Peutz-Jeghers syndrome: a report of 3 cases Authors: Odes HS;Novis BH;Barbezat GO;Bank S; Abstract: Three cases of the Peutz-Jeghers syndrome are reported and the literature is reviewed. The difficulties in the management of these patients are described and the importance of radiology and endoscopy is emphasised Link: Click to read article Title: The Peutz-Jeghers syndrome: a report of 3 cases Authors: Odes HS;Novis BH;Barbezat GO;Bank S; Abstract: Three cases of the Peutz-Jeghers syndrome are reported and the literature is reviewed. The difficulties in the management of these patients are described and the importance of radiology and endoscopy is emphasised Link: Click to read article Title: Peutz-Jeghers syndrome: its natural course and management Authors: Utsunomiya J;Gocho H;Miyanaga T;Hamaguchi E;Kashimure A; Abstract: Two hundred and twenty-two patients with Peutz-Jeghers syndrome were ascertained in Japan between 1961 and 1974 through two nationwide surveys, medical literature, and personal examinations. Genetic analysis was made of this group as well as 102 follow-up cases. The average age at diagnosis was 23 in males and 26 in females, with male to female ratio of 1:1.13. Presenting complaints of 170 patients included obstruction (42.8 per cent of patients), abdominal pain (23.4 per cent), rectal bleeding (13.5 per cent), extrusion of polyp (7.2 percent). Diagnosis of 52 patients was based on melanin pigmentation. Intussusception occurred in 46.9 per cent of the patients, most often in the small intestine. Polyps occurred in the stomach in 108 patients (48.6 per cent), small intestine, 142 patients (64 per cent), colon, 118 patients (53.2 per cent) and rectum, 71 patients (32 per cent). Among the 222 patients, cancer was histologically verified in 28. Fifteen early cancers occurred (3 gastric, 8 small intestine, 4 colon), and 11 advanced cancers (3 gastric, 1 small intestine, 6 colon, and 1 both colon and small intestine). Mortality was lower than in patients with familial polyposis coli but higher than in the general population. Conservative surgical management, planned medical follow-up, and the need for a national registration system are stressed Link: Click to read article Title: Peutz-Jeghers syndrome: its natural course and management Authors: Utsunomiya J;Gocho H;Miyanaga T;Hamaguchi E;Kashimure A; Abstract: Two hundred and twenty-two patients with Peutz-Jeghers syndrome were ascertained in Japan between 1961 and 1974 through two nationwide surveys, medical literature, and personal examinations. Genetic analysis was made of this group as well as 102 follow-up cases. The average age at diagnosis was 23 in males and 26 in females, with male to female ratio of 1:1.13. Presenting complaints of 170 patients included obstruction (42.8 per cent of patients), abdominal pain (23.4 per cent), rectal bleeding (13.5 per cent), extrusion of polyp (7.2 percent). Diagnosis of 52 patients was based on melanin pigmentation. Intussusception occurred in 46.9 per cent of the patients, most often in the small intestine. Polyps occurred in the stomach in 108 patients (48.6 per cent), small intestine, 142 patients (64 per cent), colon, 118 patients (53.2 per cent) and rectum, 71 patients (32 per cent). Among the 222 patients, cancer was histologically verified in 28. Fifteen early cancers occurred (3 gastric, 8 small intestine, 4 colon), and 11 advanced cancers (3 gastric, 1 small intestine, 6 colon, and 1 both colon and small intestine). Mortality was lower than in patients with familial polyposis coli but higher than in the general population. Conservative surgical management, planned medical follow-up, and the need for a national registration system are stressed Link: Click to read article Title: Peutz-Jeghers syndrome with pigmented oral papillomas Authors: Lowe NJ; Abstract: The association of cutaneous and mucosal pigmentation with gastrointestinal polyposis has been well-described as the Peutz-Jeghers syndrome. A case is described of a patient who has evidence of gastrointestinal polyposis, diffuse and circumscribed macular hyperpigmentation, a nasal polyp, and the additional features of buccal mucosal pigmented papillomas Link: Click to read article Title: Peutz-Jeghers syndrome Authors: Edelman MJ;Sternberg SS; Abstract: Link: Click to read article Title: Peutz-Jeghers syndrome Authors: Edelman MJ;Sternberg SS; Abstract: Link: Click to read article Title: [Petuz-Jeghers syndrome] Authors: Calderin FM;Perianes J;Melero E;Lafuente J; Abstract: Link: Click to read article Title: Peutz-Jeghers syndrome, case report Authors: Cornwell EE;Homayouni M;Blackwell F; Abstract: Link: Click to read article Title: Peutz-Jeghers syndrome. Case report with angiographic evaluation Authors: Fenlon JW;Shackelford GD; Abstract: Link: Click to read article Title: Peutz-Jeghers syndrome: clinical and roentgenographic features Authors: Godard JE;Dodds WJ;Phillips JC;Scanlon GT; Abstract: Link: Click to read article Title: The Peutz-Jeghers syndrome. Report of two cases, one with 30-year follow-up Authors: McKittrick JE;Lewis WM;Doane WA;Gerwig WH; Abstract: Link: Click to read article Title: The solitary labial lentigo. A clinicopathologic study of twenty cases Authors: Shapiro L;Zegarelli DJ; Abstract: Link: Click to read article Title: The solitary labial lentigo. A clinicopathologic study of twenty cases Authors: Shapiro L;Zegarelli DJ; Abstract: Link: Click to read article Title: Peutz-Jeghers syndrome. Involvement of the gastrointestinal and upper respiratory tracts Authors: Jancu J; Abstract: Link: Click to read article Title: Peutz-Jeghers syndrome and ureteral polyposis Authors: Sommerhaug RG;Mason T; Abstract: Link: Click to read article Title: [The Peutz-Jeghers syndrome] Authors: Palme G;von Wolff C; Abstract: Link: Click to read article
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